A case report on and chronic calcific pancreatitis primary systemic amyloidosis with symptomatic gastric involvement

Rajesh Kumar, SR Chakraborthy, A Bandopadhyay, VK Pandit, HK Bandi

Abstract


Systemic amyloidosis is a disorder characterized by extracellular deposition ofamyloid in various organs and tissues including the gastrointestinal tract, kidney, heart, and liver.Gastric involvement occurs in 8–12% of patientswith only 1% being symptomatic. Histological involvement of gastrointestinal tract baring stomach is common but is often subclinical. Moreover pancreatic involvement is also rare. Herein we report a case of a 37-year old lady patient who presented with macroglossia, periorbital purpura, abdominal symptoms and on evaluation wasdiagnosedto be having systemic amyloidosis involving stomach and chronic calcific pancreatitis.

 


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