A rare case of bullous congenital ichthyosiform erythroderma in a newborn

Thumjaa Annamalai, Vamsikrishna Reddy kandriga, Sindhu maru


Bullous congenital ichthyosiform erythroderma is a rare disorder of keratinization. It is associated with defective keratinization leading to skin fragility, blistering and hyperkeratosis. This condition was difficult to distinguish from staphylococcal scalded skin syndrome. We report a case of Bullous congenital ichthyosiform erythroderma in a 72 hour old male baby and discussed the differential diagnosis and management of the disease.

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